This page from Great Ormond Street Hospital (GOSH) explains the causes, symptoms and treatment of metopic craniosynostosis (also … What is metopic synostosis? 2009 Sep. 20(5):1439-44. . This type affects the metopic suture, which runs from the top of the head down the middle of the forehead to the bridge of the nose. The metopic suture begins at the nose and continues superiorly to meet the sagittal suture. Children with operated metopic synostosis performed significantly worse on measures of motor functioning (g w = −.45), visuospatial skills (g w = −.32), attention (g w = −.50), executive functioning (g w = −.36), arithmetic ability (g w = −.37), and behavior (g w = −.34). Also known as cranial spring surgery. 2010 May 1. The neurobehavioral morbidity of nonsyndromic trigonocephaly is incompletely understood. This corrects the abnormal triangular shape of the forehead and increases the intracranial space in the anterior fossa. The use of sagittal springs with strip craniectomy may be recommended for sagittal synostosis if the child is younger than 5 months at the time of initial surgery. Variations of endoscopic and open repair of metopic craniosynostosis. Metopic synostosis is presently the second most common form of craniosynostosis, accounting for 19% to 28% of cases 53–55 and having a prevalence of 0.9 to 2.3 per 10 000 live births. J Craniofac Surg. The purpose of this study was twofold: first, to assess the degree of developmental, educational, and behavioral problems in patients with nonsyndromic trigonocephaly and second, to establish whether patients with mild degrees of trigonocephaly had a lower frequency of such problems. Treatment involves releasing the suture and expanding and rounding out the upper face, forehead and skull. Surgical therapy for true metopic synostosis involves a fronto-orbital advancement which allows for widening the skull at the temporal fossa. Children with metopic, unicoronal and lambdoid synostosis tended to score lower on most measures than those with sagittal fusion (P<.001 to .82). Miraoui H, Ringe J, Haupl T, Marie PJ. ... Study how the condition affects learning and behavior; ... Fronto-orbital surgery for metopic and unilateral coronal synostosis. Increased EFG- and PDGFalpha-receptor signaling by mutant FGF-receptor 2 contributes to osteoblast dysfunction in Apert craniosynostosis. 19(9):1678-89. . Metopic craniosynostosis results in a narrow, triangular forehead with pinching of the temples laterally. The records of 36 consecutive children with metopic synostosis followed at one craniofacial center from 1978 to 1993 were reviewed and parental questionnaires were completed to establish the frequency of mental retardation, learning disabilities, and behavioral problems associated with this synostosis. Hum Mol Genet. Object. 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